Tratamientos respiratorios en la enfermedad neuromuscular.
Por:
Martínez Carrasco C, Cols M, Salcedo Posadas A, Sardon Prado O, Asensio de la Cruz O and Torrent Vernetta A
Publicada:
1 oct 2014
Ahead of Print:
2 jun 2014
Categoría:
Pediatrics, Perinatology and Child Health
Resumen:
In a previous article, a review was presented of the respiratory pathophysiology of the patient with neuromuscular disease, as well as their clinical evaluation and the major complications causing pulmonary deterioration. This article presents the respiratory treatments required to preserve lung function in neuromuscular disease as long as possible, as well as in special situations (respiratory infections, spinal curvature surgery, etc.). Special emphasis is made on the use of non-invasive ventilation, which is changing the natural history of many of these diseases. The increase in survival and life expectancy of these children means that they can continue their clinical care in adult units. The transition from pediatric care must be an active, timely and progressive process. It may be slightly stressful for the patient before the adaptation to this new environment, with multidisciplinary care always being maintained.
Filiaciones:
Martínez Carrasco C:
Sección de Neumología Pediátrica, Hospital Universitario La Paz, Madrid, España.
Cols M:
Sección de Neumología Pediátrica, Hospital Sant Joan de Déu, Barcelona, España
Salcedo Posadas A:
Sección de Neumología Pediátrica, Hospital Universitario Gregorio Marañón, Madrid, España
Sardon Prado O:
Sección de Neumología Pediátrica, Hospital Universitario Donostia, San Sebastián, Guipúzcoa, España
Asensio de la Cruz O:
Sección de Neumología Pediátrica, Hospital de Sabadell, Corporació Sanitària i Universitària Parc Taulí, Sabadell, Barcelona, España
Torrent Vernetta A:
Sección de Neumología Pediátrica, Hospital Universitario Vall d'Hebron, Barcelona, España
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