Fratricide-resistant CD1a-specific CAR T cells for the treatment of cortical T-cell acute lymphoblastic leukemia.


Por: Sánchez-Martínez D, Baroni ML, Gutierrez-Agüera F, Roca-Ho H, Blanch-Lombarte O, González-García S, Torrebadell-Burriel M, Junca J, Ramírez-Orellana M, Velasco-Hernández T, Bueno C, Fuster JL, Prado JG, Calvo J, Uzan B, Cools J, Camós-Guijosa M, Pflumio F, Toribio ML and Menéndez P

Publicada: 23 may 2019 Ahead of Print: 22 feb 2019
Resumen:
Relapsed/refractory T-cell acute lymphoblastic leukemia (T-ALL) has a dismal outcome, and no effective targeted immunotherapies for T-ALL exist. The extension of chimeric antigen receptor (CAR) T cells (CARTs) to T-ALL remains challenging because the shared expression of target antigens between CARTs and T-ALL blasts leads to CART fratricide. CD1a is exclusively expressed in cortical T-ALL (coT-ALL), a major subset of T-ALL, and retained at relapse. This article reports that the expression of CD1a is mainly restricted to developing cortical thymocytes, and neither CD34(+) progenitors nor T cells express CD1a during ontogeny, confining the risk of on-target/off-tumor toxicity. We thus developed and preclinically validated a CD1a-specific CAR with robust and specific cytotoxicity in vitro and antileukemic activity in vivo in xenograft models of coT-ALL, using both cell lines and coT-ALL patient-derived primary blasts. CD1a-CARTs are fratricide resistant, persist long term in vivo (retaining antileukemic activity in re-challenge experiments), and respond to viral antigens. Our data support the therapeutic and safe use of fratricide-resistant CD1a-CARTs for relapsed/refractory coT-ALL.

Filiaciones:
Sánchez-Martínez D:
 Josep Carreras Leukemia Research Institute, Department of Biomedicine, School of Medicine, University of Barcelona, Barcelona, Spain

 dsanchez

Baroni ML:
 Josep Carreras Leukemia Research Institute, Department of Biomedicine, School of Medicine, University of Barcelona, Barcelona, Spain

Gutierrez-Agüera F:
 Josep Carreras Leukemia Research Institute, Department of Biomedicine, School of Medicine, University of Barcelona, Barcelona, Spain

Roca-Ho H:
 Josep Carreras Leukemia Research Institute, Department of Biomedicine, School of Medicine, University of Barcelona, Barcelona, Spain

Blanch-Lombarte O:
 AIDS Research Institute IrsiCaixa, Institut d'Investigacio en Ciencies de la Salut Germans Trias i Pujol, Univ. Autonoma de Barcelona, Barcelona, Spain

González-García S:
 Centro de Biologia Molecular Severo Ochoa CSIC-UAM, Madrid, Spain

Torrebadell-Burriel M:
 Haematology Laboratory, Institut de Recerca Hospital Sant Joan de Deu, Barcelona, Centro de Investigacion Biomedica en Red de Enfermedades Raras, Instituto de Salud Carlos III, Barcelona, Spain

Junca J:
 ICO-Hospital Germans Trias i Pujol, Josep Carreras Leukaemia Research Institute, Universitat Autonoma de Barcelona, Badalona, Spain

Ramírez-Orellana M:
 Department of Pediatric Hematology and Oncology, Hospital Infantil Universitario Nino Jesus, Universidad Autonoma de Madrid, Madrid, Spain

Velasco-Hernández T:
 Josep Carreras Leukemia Research Institute, Department of Biomedicine, School of Medicine, University of Barcelona, Barcelona, Spain

Bueno C:
 Josep Carreras Leukemia Research Institute, Department of Biomedicine, School of Medicine, University of Barcelona, Barcelona, Spain

Fuster JL:
 Seccion de Oncohematologia Pediatrica, Hospital Clinico Universitario Virgen de la Arrixaca, Instituto Murciano de Investigacion Biosanitaria (IMIB), Murcia, Spain

Prado JG:
 AIDS Research Institute IrsiCaixa, Institut d'Investigacio en Ciencies de la Salut Germans Trias i Pujol, Univ. Autonoma de Barcelona, Barcelona, Spain

Calvo J:
 Univerite Paris Diderot and Universite Paris-Sud, UMR 967, INSERM, U967, Fontenay-aux-Roses, France

Uzan B:
 Univerite Paris Diderot and Universite Paris-Sud, UMR 967, INSERM, U967, Fontenay-aux-Roses, France

Cools J:
 KU Center for Human Genetics and VIB Center for Cancer Biology, Leuven, Belgium

Camós-Guijosa M:
 Haematology Laboratory, Institut de Recerca Hospital Sant Joan de Deu, Barcelona, Centro de Investigacion Biomedica en Red de Enfermedades Raras, Instituto de Salud Carlos III, Barcelona, Spain

Pflumio F:
 Univerite Paris Diderot and Universite Paris-Sud, UMR 967, INSERM, U967, Fontenay-aux-Roses, France

Toribio ML:
 Centro de Biologia Molecular Severo Ochoa CSIC-UAM, Madrid, Spain

Menéndez P:
 Josep Carreras Leukemia Research Institute, Department of Biomedicine, School of Medicine, University of Barcelona, Barcelona, Spain
ISSN: 00064971





BLOOD
Editorial
ELSEVIER, RADARWEG 29, 1043 NX AMSTERDAM, NETHERLANDS, Estados Unidos America
Tipo de documento: Article
Volumen: 133 Número: 21
Páginas: 2291-2304
WOS Id: 000468756600011
ID de PubMed: 30796021
imagen Open Access

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