CAR-T cells targeting CCR9 and CD1a for the treatment of T cell acute lymphoblastic leukemia.


Por: Tirado N, Fidyt K, Mansilla MJ, Garcia-Perez A, Martínez-Moreno A, Vinyoles M, Alcain J, García-Peydró M, Roca-Ho H, Fernandez-Fuentes N, Guerrero-Murillo M, Falgàs A, Velasco-Hernandez T, Bueno C, Panelli P, Mulens-Arias V, Apostolov A, Engel P, González EA, Vick B, Jeremias I, Caye-Eude A, Baruchel A, Cavé H, Genescà E, Ribera J, Díaz-Beyá M, Martínez-Sánchez MV, Fuster JL, Escudero López A, Minguillón J, Pérez-Martínez A, Ramírez-Orellana M, Torrebadell-Burriel M, Díaz VM, Toribio ML, Sánchez-Martínez D and Menéndez P

Publicada: 1 jul 2025 Ahead of Print: 1 jul 2025
Resumen:
T cell acute lymphoblastic leukemia (T-ALL) is an aggressive malignancy characterized by high rates of induction failure and relapse, and effective targeted immunotherapies are lacking. Despite promising clinical progress with genome-edited CD7-directed CAR-T cells, which present significant logistical and regulatory issues, CAR-T cell therapy in T-ALL remains challenging due to the shared antigen expression between malignant and healthy T cells. This can result in CAR-T cell fratricide, T cell aplasia, and the potential for blast contamination during CAR-T cell manufacturing. Recently described CAR-T cells target non-pan-T antigens, absent on healthy T cells but expressed on specific T-ALL subsets. These antigens include CD1a (NCT05679895), which is expressed in cortical T-ALL, and CCR9. We show that CCR9 is expressed on >70% of T-ALL patients (132/180) and is maintained at relapse, with a safe expression profile in healthy hematopoietic and non-hematopoietic tissues. Further analyses showed that dual targeting of CCR9 and CD1a could benefit T-ALL patients with a greater blast coverage than single CAR-T cell treatments. We therefore developed, characterized, and preclinically validated a novel humanized CCR9-specific CAR with robust and specific antileukemic activity as a monotherapy in vitro and in vivo against cell lines, primary T-ALL samples, and patient-derived xenografts. Importantly, CCR9/CD1a dual-targeting CAR-T cells showed higher efficacy than single-targeting CAR-T cells, particularly in T-ALL cases with phenotypically heterogeneous leukemic populations. Dual CD1a/CCR9 CAR-T therapy may prevent T cell aplasia and obviate the need for allogeneic transplantation and regulatory-challenging genome engineering approaches in T-ALL.

Filiaciones:
Tirado N:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

Fidyt K:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

Mansilla MJ:
 OneChain Immunotherapeutics S.L, Barcelona, Spain

Garcia-Perez A:
 OneChain Immunotherapeutics S.L, Barcelona, Spain

Martínez-Moreno A:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

Vinyoles M:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

Alcain J:
 Centro de Biologia Molecular Severo Ochoa CSIC-UAM, Madrid, Spain

García-Peydró M:
 Centro de Biologia Molecular Severo Ochoa CSIC-UAM, Madrid, Spain

Roca-Ho H:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

Fernandez-Fuentes N:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

Guerrero-Murillo M:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

Falgàs A:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

 Centro de Investigación Biomédica en Red de Cáncer (CIBERONC), Madrid, Spain

Velasco-Hernandez T:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

 Department of Biomedicine, School of Medicine, University of Barcelona, Barcelona, Spain

Bueno C:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

 Centro de Investigación Biomédica en Red de Cáncer (CIBERONC), Madrid, Spain

Panelli P:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

Mulens-Arias V:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

Apostolov A:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

Engel P:
 Department of Biomedicine, School of Medicine, University of Barcelona, Barcelona, Spain

González EA:
 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

 Department of Immunology, Hospital Clínic de Barcelona, Barcelona, Spain

Vick B:
 Research Unit Apoptosis in Hematopoietic Stem Cells, Helmholtz Munich, German Research Center for Environmental Health (HMGU), Munich, Germany

Jeremias I:
 Research Unit Apoptosis in Hematopoietic Stem Cells, Helmholtz Munich, German Research Center for Environmental Health (HMGU), Munich, Germany

 Department of Pediatrics, Dr. von Hauner Children's Hospital, LMU University Hospital, LMU Munich, Munich, Germany

Caye-Eude A:
 Department of Genetics, University Hospital Robert Debré

 INSERM Institut de Recherche Saint Louis, Paris, France

Baruchel A:
 Department of Genetics, University Hospital Robert Debré

 INSERM Institut de Recherche Saint Louis, Paris, France

Cavé H:
 Department of Genetics, University Hospital Robert Debré

 INSERM Institut de Recherche Saint Louis, Paris, France

Genescà E:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

Ribera J:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Department of Hematology, Institut Català d'Oncologia-Hospital Germans Trias i Pujol, Badalona, Spain

Díaz-Beyá M:
 Department of Hematology, Hospital Clínic de Barcelona, Barcelona, Spain

Martínez-Sánchez MV:
 Immunology Service, Clinical University Hospital Virgen de la Arrixaca, Instituto Murciano de Investigación Sanitaria (IMIB), University of Murcia, Murcia, Spain

Fuster JL:
 Sección de Oncohematología Pediátrica, Hospital Clínico Universitario Virgen de la Arrixaca

 Instituto Murciano de Investigación Sanitaria (IMIB), University of Murcia, Murcia, Spain

Escudero López A:
 Department of Genetics, Institute of Medical and Molecular Genetics (INGEMM), La Paz University Hospital, Madrid, Spain

Minguillón J:
 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

 CIBERER-ISCIII, IdiPAZ-CNIO Translational Research Unit in Pediatric Hemato-Oncology, La Paz University Hospital Research Institute

 Spanish National Cancer Center, Madrid, Spain

 Advanced Therapies Mixed Unit, CIEMAT/IIS-FJD, Madrid, Spain

Pérez-Martínez A:
 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

 CIBERER-ISCIII, IdiPAZ-CNIO Translational Research Unit in Pediatric Hemato-Oncology, La Paz University Hospital Research Institute

 Spanish National Cancer Center, Madrid, Spain

 Advanced Therapies Mixed Unit, CIEMAT/IIS-FJD, Madrid, Spain

 Pediatric Hemato-Oncology Department, La Paz University Hospital, Madrid, Spain

Ramírez-Orellana M:
 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

 Hospital Infantil Universitario Niño Jesús, Instituto de Investigación Sanitaria La Princesa, Madrid, Spain

Torrebadell-Burriel M:
 Institut de Recerca Pediàtrica Sant Joan de Déu

 Department of Hematology, Hospital Sant Joan de Déu, Barcelona, Spain

Díaz VM:
 OneChain Immunotherapeutics S.L, Barcelona, Spain

 Universitat Internacional de Catalunya, Sant Cugat del Vallès, Spain

Toribio ML:
 Centro de Biologia Molecular Severo Ochoa CSIC-UAM, Madrid, Spain

Sánchez-Martínez D:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

 Aragon Health Research Institute (IIS Aragon), Zaragoza, Spain

 Aragon Foundation for Research & Development (ARAID), Zaragoza, Spain

:
 Josep Carreras Leukaemia Research Institute (IJC), Barcelona, Spain

 Red Española de Terapias Avanzadas (TERAV+), Instituto de Salud Carlos III, Madrid, Spain

 Centro de Investigación Biomédica en Red de Cáncer (CIBERONC), Madrid, Spain

 Department of Biomedicine, School of Medicine, University of Barcelona, Barcelona, Spain

 Institució Catalana de Recerca i Estudis Avançats (ICREA), Barcelona, Spain

 Institut de Recerca Hospital Sant Joan de Déu-Pediatric Cancer Center Barcelona (SJD-PCCB), Barcelona, Spain
ISSN: 17568722





Journal of Hematology & Oncology
Editorial
BMC, CAMPUS, 4 CRINAN ST, LONDON N1 9XW, ENGLAND, Reino Unido
Tipo de documento: Article
Volumen: 18 Número: 1
Páginas: 69-69
WOS Id: 001521115700001
ID de PubMed: 40598348
imagen Green Published, Green Submitted, gold

MÉTRICAS