Cysteamine (Cystagon®) adherence in patients with cystinosis in Spain: successful in children and a challenge in adolescents and adults.
Por:
Ariceta G, Lara E, Camacho Díaz JA, Oppenheimer F, Vara J, Santos F, Muñoz MA, Cantarell C, Gil Calvo M, Romero R, Valenciano B, García-Nieto V, Sanahuja MJ, Crespo J, Justa ML, Urisarri A, Bedoya R, Bueno A, Daza A, Bravo J, Llamas F and Jiménez Del Cerro LA
Publicada:
1 mar 2015
Ahead of Print:
26 oct 2014
Categoría:
Medicine (miscellaneous)
Resumen:
Cysteamine has improved survival and prognosis in cystinosis. Increasing numbers of patients reach adulthood and face new challenges such as compliance that wanes over time. The aim of this study was to evaluate adherence to cysteamine treatment in a group of cystinotic patients in Spain in an attempt to identify potential therapy pitfalls and improve the overall care of affected individuals. Despite the impact of cysteamine on prognosis, there is a paucity of data regarding adherence.
Filiaciones:
Ariceta G:
Hospital Universitari Vall d' Hebron, Barcelona, Spain Hospital Universitario Cruces, Bilbao, Spain
Lara E:
Hospital Universitari Vall d' Hebron, Barcelona, Spain
Camacho Díaz JA:
Hospital Sant Joan de Déu, Barcelona, Spain
Oppenheimer F:
Hospital Universitari Clínic, Barcelona, Spain
Vara J:
Hospital Universitario 12 de Octubre, Madrid, Spain
Santos F:
Hospital Universitario Central de Asturias y Universidad de Oviedo, Oviedo, Spain
Muñoz MA:
Hospital Universitario Virgen de la Salud, Toledo, Spain
Cantarell C:
Hospital Universitari Vall d' Hebron, Barcelona, Spain
Gil Calvo M:
Complexo Hospitalario Universitario de Santiago de Compostela, Santiago de Compostela, Spain
Romero R:
Complexo Hospitalario Universitario de Santiago de Compostela, Santiago de Compostela, Spain
Valenciano B:
Hospital Universitario Materno-Infantil Las Palmas, Las Palmas de Gran Canaria, Spain
García-Nieto V:
Hospital Universitario Ntra. Sra. de la Candelaria, Santa Cruz de Tenerife, Spain
Sanahuja MJ:
Hospital Universitario La Fe, Valencia, Spain
Crespo J:
Hospital Universitario Dr Peset, Valencia, Spain
Justa ML:
Hospital Universitario Miguel Servet, Zaragoza, Spain
Urisarri A:
Hospital Arquitecto Marcide, Ferrol, Spain
Bedoya R:
Hospital Universitario Virgen del Rocío, Sevilla, Spain
Bueno A:
Hospital Universitario Materno-Infantil, Materno-Infantil Carlos Haya, Málaga, Spain
Daza A:
Complejo Hospitalario de Torrecárdenas, Almería, Spain
Bravo J:
Hospital Universitario Virgen de las Nieves, Granada, Spain
Llamas F:
Hospital General de Albacete, Albacete, Spain
Jiménez Del Cerro LA:
Hospital General Universitario de Alicante, Alicante, Spain
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